Abstract: CHILBLAIN LUPUS ERYTHEMATOSUS IN A MONOLYGOTE TWIN.#C. Chams, M. Akbarian, P. Mansoori, F. Shahram, and F. Davatchi#Revista Espanola de Reumatologia, 1993; 20 (Suppl 1): p. 358 #Chilblain lupus erythematosus or lupus pernio was described by HUTCHINSON in 1888. Even actually it is difficult to put this entity in a well defined nosologic place as systemic lupus erythematosus. We report here the case of a twin monozygote brothers of 11 years old, ...
Abstract: Behcet's disease (BD) is not rare in children, and it's clinical picture differs from that in adults. We studied 66 patients in whom the disease was diagnosed under the age 16 from a population of 2068 BD patients. Comparison of the results with the adults by the student paired t test showed: although the most frequent initial manifestation of BD in children was oral aphthosis (54.5%), it was less frequent ...
Abstract: The annual incidence of Behcet's Disease (BD) is as high as 300 patients per year. The mean age at the onset of the first symptom is 26.7 years (SD = 9.7). The sex distribution is 54% male and 46% female. The initial manifestation was mainly oral aphthosis (73%), uveitis (13%), genital ulcerations (11%), arthritis (9%), and skin manifestations (9%). Clinical manifestations were as fallow: mucous membrane manifestations were seen in 95.5% ...
Abstract: There is only three reports on the frequency of audio vestibular involvement in BD in the literature. In these studies, done in small population of BD patients, the frequency of auditory involvement were reported as high as 60%, and the vestibular involvement between 25 to 37%. We studied prospectively the audio vestibular involvement in 80 patients with BD, and compared them with 102 controls (CG) including hospital staffs, patients with ...
Abstract: An increased rate of infection among SLE patients has long been reported from western countries. In a retrospective study in 893 patients, we analyzed 203 cases who had one or more episodes of infection between 1974 and 1992. Among them 181 were females and 22 were males (89% female) . The diagnosis of infection was established by both clinical and laboratory findings. Almost more than half of the infections were ...
Abstract: No fewer than five sets of diagnostic criteria for Behcet's disease are currently in use. The International Study Group have therefore undertaken an extensive study of existing criteria and have developed recommended new international criteria based on the collection of data from 914 patients with Behcet's disease and 308 controls, of whom 886 (97%) and 97 respectively had mouth ulceration. It is recommended that these new criteria should replace the ...
Abstract: Results of PCP are well known in lupus nephritis. We present here it's outcome in patients with early stage of WH0 type IV lupus nephritis. The criteria for selection was a serum creatinine inferior to 1.3 mg/ 100 ml and a minimum follow up time of 18 months. 35 patients fulfilled the selection criteria. proteinuria, hematuria, leucocyturia, cast, BUN, creatinine, and blood pressure were measured before PCP and after each one. ...
Abstract: Since our first report in 1987 to the 11th EULAR congress of rheumatology several reports had shown the efficacy of PCP in posterior uveitis (PU) and retinal vasculitis (RV) of BD. The aim of this report is to show the safety and the efficacy of PCP even in patients who have been followed for more than 2 years (49 cases) . PCP was given as 1g/m2/body surface, once per month, ...
Abstract: Systemic Lupus Erythematosus (SLE) is a rather frequent disease in Iran. In the past 13 years, 449 patients with SLE attended the SLE clinic. Lupus nephritis was discovered in 278 of them. The purpose of this study is to demonstrate the caracteristics of lupus nephritis in Iran (percentage of proteinuria, hematuria, leucocyturia, casts, renal insufficiency, hypertension, and patterns of renal biopsy), to compare them to the remaining patients with SLE ...
Abstract: The evaluation of the inflammatory state of Behcet`s Disease and it's quantification is most difficult. The difficulty is due to the recurrent attacks and spontaneous remissions that characterizes the disease. In IBDDAM the patients is evaluated on several weeks or months. Each attack is measured separately and given an index. The obtained indexes are added together and the total is divided by the number of months of the evaluation period. ...